Table of Contents

 

 

 

 

Introduction

1

1

Orbit

3

 

Trauma

3

 

Blunt Trauma

3

 

Orbital Contusion

3

 

Orbital Hemorrhage/Orbital Compartment Syndrome

4

 

Orbital Fractures

5

 

Penetrating Trauma

8

 

Intraorbital Foreign Body

8

 

Globe Subluxation

9

 

Carotid-Cavernous and Dural Sinus Fistulas

10

 

Infections

12

 

Preseptal Cellulitis

12

 

Orbital Cellulitis

13

 

Inflammation

15

 

Thyroid-Related Ophthalmopathy

15

 

Idiopathic Orbital Inflammation (Orbital Pseudotumor)

18

 

Congenital Anomalies

19

 

Congenital Anophthalmia

19

 

Microphthalmos

20

 

Microphthalmos with Cyst

20

 

Nanophthalmos

20

 

Craniofacial Disorders

20

 

Pediatric Orbital Tumors

21

 

Benign Pediatric Orbital Tumors

21

 

Orbital Dermoid (Dermoid Cyst)

21

 

Lymphangioma

21

 

Juvenile Xanthogranuloma

22

 

Histiocytic Tumors

23

 

Malignant Pediatric Orbital Tumors

23

 

Rhabdomyosarcoma

23

 

Neuroblastoma

24

 

Leukemia

24

 

Adult Orbital Tumors

26

 

Benign Adult Orbital Tumors

26

 

Cavernous Hemangioma

26

 

Mucocele

26

 

Neurilemoma (Schwannoma)

27

 

Meningioma

28

 

Fibrous Histiocytoma

28

 

Fibro-Osseous Tumors

29

 

Cholesterol Granuloma

29

 

Aneurysmal Bone Cyst

29

 

Malignant Adult Orbital Tumors

29

 

Lymphoid Tumors

29

 

Fibro-Osseous Tumors

30

 

Metastatic Tumors

31

 

Acquired Anophthalmia

31

 

Atrophia Bulbi and Phthisis Bulbi

32

 

Atrophia Bulbi without Shrinkage

32

 

Atrophia Bulbi with Shrinkage

32

 

Atrophia Bulbi with Disorganization (Phthisis Bulbi)

32

2

Ocular Motility and Cranial Nerves

35

 

Strabismus

35

 

Phoria

35

 

Tropia

35

 

Horizontal Strabismus

37

 

Esotropia

37

 

Infantile Esotropia

37

 

Accommodative Esotropia

38

 

Acquired Nonaccommodative Esotropia and Other Forms of Esotropia

39

 

Exotropia

40

 

Basic Exotropia

40

 

Convergence Insufficiency

40

 

Pseudodivergence Excess

41

 

True Divergence Excess

41

 

A-, V-, and X-Patterns

41

 

A-Pattem

41

 

V-Pattern

42

 

X-Pattern

42

 

Vertical Strabismus

42

 

Brown’s Syndrome (Superior Oblique Tendon Sheath Syndrome)

42

 

Dissociated Strabismus Complex: Dissociated Vertical Deviation, Dissociated Horizontal Deviation, Dissociated Torsional Deviation

43

 

Monocular Elevation Deficiency (Double Elevator Palsy)

44

 

Type 1

44

 

Type 2

44

 

Type 3

44

 

Miscellaneous Strabismus

45

 

Duane’s Retraction Syndrome

45

 

Type 1

45

 

Type 2

45

 

Type 3

45

 

Möbius’ Syndrome

46

 

Restrictive Strabismus

46

 

Congenital Fibrosis Syndrome

46

 

Generalized Fibrosis (Autosomal Dominant [AD] > Autosomal Recessive [AR] > Idiopathic)

46

 

Congenital Fibrosis of Inferior Rectus (Sporadic or Familial)

46

 

Strabismus Fixus (Sporadic)

47

 

Vertical Retraction Syndrome

47

 

Congenital Unilateral Fibrosis (Sporadic)

47

 

Nystagmus

47

 

Congenital Nystagmus

47

 

Acquired Nystagmus

48

 

Physiologic Nystagmus

49

 

Third Cranial Nerve Palsy

50

 

Nuclear

51

 

Fascicular

51

 

Subarachnoid Space

51

 

Intracavernous Space

51

 

Orbital Space

51

 

Fourth Cranial Nerve Palsy

53

 

Nuclear

54

 

Fascicular

54

 

Subarachnoid Space

54

 

Intracavernous Space

54

 

Sixth Cranial Nerve Palsy

56

 

Nuclear

56

 

Fascicular

56

 

Subarachnoid Space

57

 

Petrous Space

57

 

Intracavernous Space

57

 

Multiple Cranial Nerve Palsies

58

 

Brain Stem

58

 

Subarachnoid Space

58

 

Cavernous Sinus Syndrome

59

 

Orbital Apex Syndrome

59

 

Chronic Progressive External Ophthalmoplegia

61

 

Kearns–Sayre Syndrome

61

 

Mitochondrial Encephalopathy, Lactic Acidosis, and Stroke-Like Episodes

61

 

Myoclonic Epilepsy and Ragged Red Fibers

61

 

Myotonic Dystrophy

61

 

Oculopharyngeal Muscular Dystrophy

61

 

Horizontal Motility Disorders

63

 

Internuclear Ophthalmoplegia

63

 

One-and-a-Half Syndrome

63

 

Vertical Motility Disorders

65

 

Progressive Supranuclear Palsy (Steele–Richardson–Olszewski Syndrome)

65

 

Dorsal Midbrain (Parinaud’s) Syndrome

65

 

Skew Deviation

65

 

Myasthenia Gravis

67

3

Lids, Lashes and Lacrimal System

69

 

Eyelid Trauma

69

 

Contusion

69

 

Abrasion

70

 

Avulsion

70

 

Laceration

71

 

Eyelid Infections

73

 

Blepharitis and Mcibomitis

73

 

Herpes Simplex Virus

75

 

Herpes Zoster Virus

76

 

Molluscum Contagiosum

77

 

Demodicosis

78

 

Phthiriasis or Pediculosis

78

 

Leprosy

79

 

Eyelid Inflammations

79

 

Chalazion or Hordeolum (Stye)

79

 

Contact Dermatitis

80

 

Blepharochalasis

82

 

Madarosis

82

 

Vitiligo and Poliosis

83

 

Acne Rosacea

84

 

Eyelid Malpositions

85

 

Ptosis

85

 

Aponeurotic (Involutional)

85

 

Mechanical

85

 

Myogenic

85

 

Neurogenic

86

 

Congenital

86

 

Dermatochalasis

88

 

Ectropion

89

 

Cicatricial

89

 

Congenital

89

 

Inflammatory

89

 

Involutional

89

 

Mechanical

89

 

Paralytic

89

 

Entropion

91

 

Cicatricial

91

 

Congenital

91

 

Involutional

92

 

Spastic

92

 

Blepharospasm

93

 

Essential Blepharospasm

93

 

Meige’s Syndrome

93

 

Bell’s Palsy

94

 

Floppy Eyelid Syndrome

96

 

Trichiasis

97

 

Congenital Eyelid Anomalies

99

 

Ankyloblepharon

99

 

Blepharophimosis

99

 

Coloboma

99

 

Cryptophthalmos

100

 

Distichiasis

100

 

Epiblepharon

101

 

Epicanthus

101

 

Euryblepharon

102

 

Microblepharon

102

 

Telecanthus

102

 

Benign Eyelid Tumors

103

 

Pigmented Benign Eyelid Tumors

103

 

Acquired Nevus

103

 

Ephelis (Freckle)

103

 

Oculodermal Melanocytosis (Nevus of Ota)

104

 

Seborrheic Keratosis

104

 

Squamous Papilloma

105

 

Verruca Vulgaris (Viral Papilloma)

105

 

Nonpigmented Benign Eyelid Tumors

106

 

Xanthelasma

106

 

Moll’s Gland Cyst (Hidrocystoma, Sudoriferous Cyst)

107

 

Epidermal Inclusion Cyst

107

 

Inverted Follicular Keratosis

108

 

Milia

108

 

Sebaceous (Pilar) Cyst

108

 

Pilomatrixoma (Calcifying Epithelioma of Malherbe)

109

 

Vascular Benign Eyelid Tumors

109

 

Capillary Hemangioma

109

 

Lymphangioma

110

 

Port Wine Stain (Nevus Flammeus)

110

 

Malignant Eyelid Tumors

110

 

Basal Cell Carcinoma

110

 

Squamous Cell Carcinoma

111

 

Actinic Keratosis

112

 

Keratoacanthoma

112

 

Sebaceous Cell Carcinoma

113

 

Malignant Melanoma

114

 

Merkel Cell Tumor

115

 

Metastatic Tumors

115

 

Kaposi’s Sarcoma

116

 

Systemic Diseases

116

 

Neurofibromatosis

116

 

Sarcoidosis

118

 

Amyloidosis

119

 

Canaliculitis

120

 

Dacryocystitis

121

 

Nasolacrimal Duct Obstruction

123

 

Dacryoadenitis

125

 

Lacrimal Gland Tumors

128

 

Benign Mixed Cell Tumor (Pleomorphic Adenoma)

128

 

Malignant Mixed Cell Tumor (Pleomorphic Adenocardnoma)

129

 

Adenoid Cystic Carcinoma (Cylindroma)

129

4

Conjunctiva and Sclera

131

 

Trauma

131

 

Foreign Body

131

 

Laceration

131

 

Open Globe

131

 

Subcojunctival Hemorrhage

134

 

Telangiectasia

135

 

Microancurysm

136

 

Dry Eye Disease (Dry Eye Syndrome, Keratoconjunctivitis Sicca)

136

 

Aqueous-Deficient Dry Eye

137

 

Evaporative Dry Eye

137

 

Inflammation

141

 

Chemosis

141

 

Follicles

141

 

Granuloma

142

 

Hyperemia

142

 

Membranes

142

 

Papillae

142

 

Phlyctenule

143

 

Conjunctivitis

144

 

Acute Conjunctivitis

144

 

Infectious

144

 

Gonococcal

144

 

Nongonococcal Bacterial

144

 

Adenoviral

145

 

Herpes Simplex Virus

145

 

Herpes Zoster Virus

146

 

Pediculosis

146

 

Allergic

146

 

Seasonal

146

 

Atopic Keratoconjunctivitis

146

 

Vernal Keratoconjunctivitis

147

 

Toxic

147

 

Chronic Conjunctivitis

148

 

Infectious

148

 

Chlamydial

148

 

Molluscum Contagiosum

148

 

Allergic

148

 

Perennial

148

 

Giant Papillary Conjunctivitis

149

 

Toxic

149

 

Other

149

 

Superior Limbic Keratoconjunctivitis

149

 

Kawasaki’s Disease

150

 

Ligneous

150

 

Parinaud’s Oculoglandular Syndrome

150

 

Ophthalmia Neonatorum

150

 

Degenerations

153

 

Amyloidosis

154

 

Concretions

154

 

Pinguecula

154

 

Pterygium

154

 

Ocular Cicatricial Pemphigoid

156

 

Stevens–Johnson Syndrome (Erythema Multiforme Major)

157

 

Tumors

158

 

Congenital

158

 

Hamartoma

158

 

Choristoma

159

 

Epithelial

159

 

Cysts

159

 

Papilloma

159

 

Conjunctival Intraepithelial Neoplasia

160

 

Squamous Cell Carcinoma

161

 

Melanocytic

161

 

Nevus

161

 

Ocuiar Melanocytosis

162

 

Oculodermal Melanocytosis (Nevus of Ota)

163

 

Primary Acquired Melanosis

163

 

Secondary Acquired Melanosis

163

 

Malignant Melanoma

164

 

Stromal

165

 

Cavernous Hemangioma

165

 

Juvenile Xanthogranuloma

165

 

Kaposi’s Sarcoma

165

 

Lymphangiectasis

166

 

Lymphoid

166

 

Pyogenic Granuloma

167

 

Caruncle

167

 

Episcleritis

168

 

Scleritis

169

 

Scleral Discoloration

171

 

Alkaptonuria (Ochronosis)

171

 

Ectasia (Staphyloma)

172

 

Ostcogenesis Imperfecta

172

 

Scleral Icterus

172

 

Senile Scleral Plaque

172

5

Cornea

175

 

Trauma

175

 

Abrasion

175

 

Birth Trauma

176

 

Burn

177

 

Foreign Body

178

 

Laceration

179

 

Recurrent Erosion

180

 

Peripheral Ulcerative Keratitis

180

 

Marginal Keratolysis

180

 

Mooren’s Ulcer

180

 

Staphylococcal Marginal Keratitis

180

 

Marginal Keratolysis

181

 

Mooren’s Ulcer

181

 

Staphylococcal Marginal Keratitis

182

 

Contact Lens-Related Problems

183

 

Rigid Lenses

183

 

Soft Lenses

184

 

Corneal Abrasion

185

 

Corneal Hypoxia

185

 

Contact Lens-Related Dendritic Keratitis

185

 

Contact Lens Solution Hypersensitivity or Toxicity

185

 

Corneal Neovascularization

185

 

Corneal Warpage

186

 

Damaged Contact Lens

187

 

Deposits on Contact Lens

187

 

Giant Papillary Conjunctivitis

187

 

Infectious Keratitis

188

 

Sterile Corneal Infiltrates

188

 

Poor Fit (Loose)

188

 

Poor Fit (Tight)

188

 

Superior Limbic Keratoconjunctivitis

188

 

Superficial Punctate Keratitis

188

 

Miscellaneous

189

 

Delle

189

 

Exposure Keratopathy

189

 

Filamentary Keratitis

190

 

Keratic Precipitates

190

 

Superficial Punctate Keratitis

191

 

Thygeson’s Superficial Punctate Keratitis

191

 

Corneal Edema

193

 

Graft Rejection or Failure

194

 

Infectious Keratitis (Corneal Ulcer)

196

 

Bacterial

196

 

Fungal

197

 

Parasitic

197

 

Viral

198

 

Interstitial Keratitis

203

 

Pannus

205

 

Degenerations

206

 

Arcus Senilis

206

 

Band Keratopathy

207

 

Crocodile Shagreen

207

 

Furrow Degeneration

208

 

Lipid Keratopathy

208

 

Spheroidal Degeneration (Actinic Degeneration, Labrador Keratopathy, Climatic Droplet Keratopathy, Bietti’s Nodular Dystrophy)

208

 

Salzmann’s Nodular Degeneration

208

 

Terrien’s Marginal Degeneration

209

 

White Limbal Girdle of Vogt

209

 

Ectasias

211

 

Keratoconus

211

 

Keratoglobus

212

 

Pellucid Marginal Degeneration

212

 

Congenital Anomalies

214

 

Cornea Plana

214

 

Dermoid

214

 

Haab’s Striae

215

 

Megalocornea

215

 

Microcornea

216

 

Sclerocornea

216

 

Dystrophies

218

 

Anterior (Epithelial and Bowman’s Membrane)

218

 

Anterior Basement Membrane Dystrophy (Epithelial Basement Membrane Dystrophy, Map-Dot-Fingerprint Dystrophy, Cogan’s Microcystic Dystrophy)

218

 

Gelatinous Droplike Dystrophy

218

 

Reis-Bückler Dystrophy (Honeycomb Dystrophy, Thiel-Behnke Dystrophy)

219

 

Stromal

219

 

Avellino Dystrophy

219

 

Central Cloudy Dystrophy of François

219

 

Schnyder’s Central Crystalline Dystrophy

220

 

Congenital Hereditary Stromal Dystrophy

220

 

François-Nectans Fleck (Mouchetée) Dystrophy

221

 

Granular Dystrophy

221

 

Lattice Dystrophy

221

 

Macular Dystrophy

222

 

Pre-Descemet’s Dystrophy (Deep Filiform Dystrophy)

223

 

Posterior (Endothelial)

223

 

Congenital Hereditary Endothelial Dystrophy

223

 

Fuchs’ Endothelial Dystrophy

223

 

Posterior Polymorphous Dystrophy

224

 

Metabolic Diseases

225

 

Deposits

226

 

Calcium

226

 

Copper

226

 

Cysteine (Cystinosis)

227

 

Drugs

227

 

Immunoglobulin (Multiple Mycloma)

228

 

Iron

228

 

Lipid or Cholesterol (Dyslipoproteinemias)

228

 

Melanin

229

 

Tyrosine (Tyrosinemia) Type II

229

 

Urate (Gout)

229

 

Verticillata (Vortex Keratopathy)

229

 

Enlarged Corneal Nerves

230

 

Tumors

231

6

Anterior Chamber

233

 

Primary Angle-Closure Glaucoma

233

 

Secondary Angle–Closure Glaucoma

236

 

Hypotony

238

 

Hyphema

240

 

Cells and Flare

241

 

Hypopyon

243

 

Endophthalmitis

244

 

Postoperative

244

 

Posttraumatic

244

 

Endogenous

245

 

Anterior Uveitis (Iritis Iridocyditis)

248

 

Infectious Anterior Uveitis

248

 

Herpes Simplex and Herpes Zoster Ophthalmicus

248

 

Lyme Disease

248

 

Syphilis

248

 

Tuberculosis

248

 

Noninfectious Anterior Uveitis

249

 

Nongranulomatous

249

 

Granulomatous

251

 

Uveitis-Glaucoma-Hyphema Syndrome

255

7

Iris and Pupils

257

 

Trauma

257

 

Angle Recession

258

 

Cyclodialysis

258

 

Iridodialysis

258

 

Sphincter Tears

259

 

Corectopia

261

 

Seclusio Pupillae

262

 

Peripheral Anterior Synechiae

263

 

Rubeosis Iridis

264

 

Neovascular Glaucoma

265

 

Pigment Dispersion Syndrome

266

 

Pigmentary Glaucoma

268

 

Iris Heterochromia

269

 

Heterochromia Iridis

269

 

Heterochromia Iridum

269

 

Congenital

269

 

Acquired

270

 

Anisocoria

271

 

Greater Anisocoria in Dark (Abnormal Pupil is Smaller)

271

 

Greater Anisocoria in Light (Abnormal Pupil is Larger)

271

 

Anisocoria Equal in Light and Dark

271

 

Adie’s Tonic Pupil

272

 

Argyll Robertson Pupil

274

 

Horner’s Syndrome

275

 

Central (First-Order Neuron)

275

 

Preganglionic (Second-Order Neuron)

275

 

Postganglionic (Third-Order Neuron)

275

 

Relative Afferent Pupillary Defect (Marcus Gunn Pupil)

277

 

Leukocoria

279

 

Congenital Anomalies

280

 

Aniridia

280

 

Coloboma

281

 

Persistent Pupillary Membrane

281

 

Mesodermal Dysgenesis Syndromes

282

 

Axenfeld’s Anomaly

283

 

Alagille’s Syndrome

283

 

Rieger’s Anomaly

283

 

Rieger’s Syndrome

283

 

Iridocorneal Endothelial Syndromes

285

 

Essential Iris Atrophy (Progressive Iris Atrophy)

285

 

Chandler’s Syndrome

285

 

Iris Nevus (Cogan-Reese) Syndrome

286

 

Tumors

287

 

Cyst

287

 

Nevus

288

 

Nodules

288

 

Iris Pigment Epithelium Tumors

290

 

Juvenile Xanthogranuloma

290

 

Malignant Melanoma

290

 

Metastatic Tumors

291

8

Lens

293

 

Congenital Anomalies

293

 

Coloboma

293

 

Lenticonus

294

 

Lentiglobus

294

 

Microspherophakia

294

 

Mittendorf Dot

295

 

Congenital Cataract

296

 

Capsular

296

 

Lamellar or Zonular

296

 

Lenticular or Nuclear

296

 

Polar

297

 

Sutural

297

 

Hereditary or Syndromes

297

 

Intrauterine Infections

298

 

Metabolic

298

 

Ocular Disorders

298

 

Other

299

 

Acquired Cataract

300

 

Cortical Degeneration

300

 

Nuclear Sclerosis

301

 

Subcapsular Cataract

302

 

Senile

303

 

Systemic Disease

303

 

Other Eye Diseases

304

 

Toxic

305

 

Trauma

305

 

Posterior Capsular Opacification (Secondary Cataract)

306

 

Aphakia

308

 

Pseudophakia

309

 

Exfoliation

310

 

Pseudoexfoliation Syndrome

311

 

Pseudoexfoliation Glaucoma

312

 

Lens-Induced Glaucoma

314

 

Lens Particle

314

 

Phacolytic

314

 

Phacomorphic

314

 

Dislocated Lens (Ectopia Lentis)

316

 

Ectopia Lentis Et Pupillae (Autosomal Recessive)

316

 

Homocystinuria (Autosomal Recessive)

316

 

Hyperlysinemia

316

 

Marfan’s Syndrome (Autosomal Dominant)

316

 

Microspherophakia

317

 

Simple Ectopia Lentis (Autosomal Dominant)

317

 

Sulfite Oxidase Deficiency (Autosomal Recessive)

317

 

Other

317

9

Vitreous

319

 

Amyloidosis

319

 

Asteroid Hyalosis

320

 

Persistent Hyperplastic Primary Vitreous (Persistent Fetal Vasculature Syndrome)

321

 

Posterior Vitreous Detachment

323

 

Synchesis Scintillans

324

 

Vitreous Hemorrhage

324

 

Vitritis

326

10

Retina and Choroid

327

 

Trauma

328

 

Choroidal Rupture

328

 

Commotio Retinae (Berlin’s Edema)

32h

 

Purtscher’s Retinopathy

329

 

Traumatic Retinal Breaks

330

 

Chorioretinitis Sclopetaria

331

 

Hemorrhages

331

 

Preretinal Hemorrhage

331

 

Intraretinal Hemorrhage

331

 

Subretinal Hemorrhage

333

 

Cotton-Wool Spot

333

 

Branch Retinal Artery Occlusion

334

 

Central Retinal Artery Occlusion

336

 

Ophthalmic Artery Occlusion

339

 

Branch Retinal Vein Occlusion

340

 

Central/Hemiretinal Vein Occlusion

342

 

Venous Stasis Retinopathy

346

 

Ocular Ischemic Syndrome

346

 

Retinopathy of Prematurity

348

 

Coats’ Disease/Leber’s Miliary Aneurysms

350

 

Eales’ Disease

352

 

Idiopathic Juxtafoveal Retinal Telangiectasia

352

 

Type 1a (Unilateral Congenital Parafoveal Telangiectasia)

353

 

Type 1B (Unilateral Idiopathic Parafoveal Telangiectasia)

353

 

Type 2 (Bilateral Acquired Parafoveal Telangiectasia)

353

 

Type 3 (Bilateral Perifoveal Telangiectasis with Capillary Obliteration)

354

 

Retinopathies Associated with Blood Abnormalities

354

 

Retinopathy of Anemia

354

 

Leukemic Retinopathy

355

 

Sickle Cell Retinopathy

356

 

Diabetic Retinopathy

357

 

Insulin-Dependent Diabetes (Type I)

357

 

Non-Insulin-Dependent Diabetes (Type Ii)

358

 

Non-Proliferative Diabetic Retinopathy

358

 

Proliferative Diabetic Retinopathy

360

 

Hypertensive Retinopathy

363

 

Toxemia of Pregnancy

364

 

Acquired Retinal Arterial Macroaneurysm

365

 

Radiation Retinopathy

366

 

Age-Related Macular Degeneration

367

 

Non-Exudative (Dry) Macular Degeneration

368

 

Exudative (Wet) Macular Degeneration

370

 

Retinal Angiomatous Proliferation

374

 

Polypoidal Choroidal Vasculopathy

375

 

Myopic Degeneration/Pathologic Myopia

377

 

Angioid Streaks

379

 

Central Serous Chorioretinopathy (Idiopathic Central Serous Choroidopathy)

381

 

Cystoid Macular Edema

383

 

Macular Hole

385

 

Epiretinal Membrane/Macular Pucker

388

 

Myelinated Nerve Fibers

390

 

Solar/Photic Retinopathy

391

 

Toxic (Drug) Maculopathies

392

 

Aminoglycosides (Gentamkin/Tobramicin/Amikacin)

392

 

Canthaxanthine (Orobronze)

392

 

Chloroquine (Aralen)/Hydroxychloroquine (Plaquenil)

392

 

Chlorpromazine (Thorazine)

394

 

Deferoxamine (Desferal)

394

 

Interferon-Alpha

394

 

Methoxyflurane (Penthrane)

394

 

Niacin

395

 

Quinine (Quinamm)

395

 

Sildenafil (Viagra)

396

 

Tadalafil (Cialis)/Vardenafil (Levitra)

396

 

Talc

396

 

Tamoxifen (Nolvadex)

396

 

Thioridazine (Mellaril)

397

 

Lipid Storage Diseases

397

 

Farber’s Disease (Glycolipid)

398

 

Mucolipidosis (Mucopolysaccharidoses)

398

 

Niemann–Pick Disease (Ceramide Phosphaddyl Choline)

398

 

Sandhoff’s Disease (Gangliosidosis Type II)

398

 

Tay—Sachs Disease (Gangliosidosis Type I)

398

 

Peripheral Retinal Degenerations

398

 

Lattice Degeneration

398

 

Pavingstone (Cobblestone) Degeneration

399

 

Peripheral Cystoid Degeneration

400

 

Snail Track Degeneration

400

 

Retinoschisis

400

 

Retinal Detachment

403

 

Rhegmatogenous Retinal Detachment

403

 

Serous (Exudative) Retinal Detachment

404

 

Traction Retinal Detachment

405

 

Choroidal Detachment

407

 

Choroidal Effusion

407

 

Choroidal Hemorrhage

407

 

Chorioretinal Folds

408

 

Chorioretinal Coloboma

409

 

Proliferative Vitreoretinopathy

410

 

Intermediate Uveitis/Pars Planitis

411

 

Neuroretinitis (Leber’s Idiopathic Stellate Neuroretinitis)

412

 

Posterior Uveitis: Infections

414

 

Acute Retinal Necrosis

414

 

Candidiasis

415

 

Cysticercosis

416

 

Cytomegalovirus

416

 

Diffuse Unilateral Subacute Neuroretinitis

418

 

Human Immunodeficiency Virus

419

 

Pneumocystis Carinii Choroidopathy

419

 

Presumed Ocular Histoplasmosis Syndrome

420

 

Progressive Outer Retinal Necrosis Syndrome

421

 

Rubella

422

 

Syphilis (Luetic Chorioretinitis)

422

 

Toxocariasis

423

 

Toxoplasmosis

424

 

Tuberculosis

426

 

Posterior Uveitis: White Dot Syndromes

426

 

Acute Macular Neuroretinopathy

426

 

Acute Posterior Multifocal Placoid Pigment Epitheliopathy

426

 

Acute Retinal Pigment Epitheliitis (Krill’s Disease)

428

 

Birdshot Choroidopathy (Vitiliginous Chorioretinitis)

429

 

Multifocal Choroiditis and Panuveitis/Subretinal Fibrosis and Uveitis Syndrome

430

 

Punctate Inner Choroidopathy

430

 

Multiple Evanescent White Dot Syndrome

431

 

Acute Idiopathic Blind Spot Enlargement Syndrome

432

 

Posterior Uveitis: Other Inflammatory Disorders

432

 

Behçet’s Disease

432

 

Idiopathic Uveal Effusion Syndrome

433

 

Masquerade Syndromes

434

 

Posterior Scleritis

435

 

Sarcoidosis

436

 

Serpiginous Choroidopathy (Geographic Helicoid Peripapillary Choroidopathy)

437

 

Sympathetic Ophthalmia

438

 

Vogt–Koyanagi–Harada Syndrome/Harada’s Disease

439

 

Posterior Uveitis: Evaluation/Management

440

 

Hereditary Chorioretinal Dystrophies

442

 

Central Areolar Choroidal Dystrophy

442

 

Choroideremia

443

 

Congenital Stationary Night Blindness

444

 

Crystalline Retinopathy of Bietti

446

 

Gyrate Atrophy

446

 

Progressive Cone Dystrophy

447

 

Rod Monochromatism (Achromatopsia)

448

 

Hereditary Macular Dystrophies

448

 

Adult Foveomacular Vitelliform Dystrophy

448

 

Best’s Disease

448

 

Butterfly Pattern Dystrophy

451

 

Dominent Drusen (Doyne’s Honeycomb Dystrophy, Malattia Leventinese)

451

 

North Carolina Macular Dystrophy (Lefler-Wadsworth-Sidbury Dystrophy)

452

 

Pseudoinilammatory Macular Dystrophy (Sorsby’s Dystrophy)

453

 

Sjögren Reticular Pigment Dystrophy

453

 

Stargardt’s Disease/Fundus Flavimaculatus

453

 

Hereditary Vitreoretinal Degenerations

454

 

Familial Exudative Vitreoretinopathy

454

 

Enhanced S-Cone Syndrome/Goldmann–Favre Syndrome

456

 

Marshall Syndrome

456

 

Snowflake Degeneration

456

 

Wagner/Jansen/Stickler Vitreoretinal Dystrophies

456

 

Leber’s Congenital Amaurosis

458

 

Retinitis Pigmentosa

459

 

Atypical Forms

459

 

Retinitis Pigmentosa Inversus

459

 

Retinitis Pigmentosa Sine Pigmento

459

 

Retinitis Punctata Albescens

459

 

Sector Retinitis Pigmentosa

459

 

Forms Associated with Systemic Abnormalities

459

 

Abetalipoproteinemia (Bassen-Kornzweig Syndrome)

459

 

Alstrom’s Disease

459

 

Cockayne’s Syndrome

460

 

Kearns–Sayre Syndrome

460

 

Laurence–Moon/Bardet–Biedl Syndromes

460

 

Neuronal Ceroid Lipofuscinosis (Batten Disease)

461

 

Refsum’s Disease

461

 

Usher’s Syndrome

461

 

Albinism

464

 

Ocular Albinism

464

 

Oculocutaneous Albinism

464

 

Phakotnatoses

465

 

Angiomatosis Retinae (Von Hippel-Lindau Disease)

465

 

Ataxia Telangiectasia (Louis-Bar Syndrome)

465

 

Encephalotrigeminal Angiomatosis (Sturge-Weber Syndrome)

466

 

Neurofibromatosis (Von Recklinghausen’s Disease)

466

 

Racemose Hemangiomiitosis (Wyburn–Mason Syndrome)

467

 

Tuberous Sclerosis (Bourneville’s Disease)

467

 

Tumors

468

 

Benign Choroidal Tumors

468

 

Choroidal Hemangioma

468

 

Choroidal Nevus

470

 

Choroidal Osteoma

470

 

Benign Retinal Tumors

471

 

Astrocytic Hamartoma

471

 

Capillary Hemangioma

471

 

Cavernous Hemangioma

472

 

Congenital Hypertrophy of the Retinal Pigment Epithelium

473

 

Bear Tracks

474

 

Combined Hamartoma of Retinal Pigment Epithelium and Retina

475

 

Malignant Tumors

475

 

Choroidal Malignant Melanoma

475

 

Choroidal Metastasis

477

 

Primary Intraocular Lymphoma (Reticulum Cell Sarcoma)

479

 

Retinoblastoma

479

 

Paraneoplastic Syndromes

480

 

Bilateral Diffuse Uveal Melanocytic Proliferation Syndrome

480

 

Carcinoma-Associated Retinopathy

480

 

Cutaneous Melanoma-Associated Retinopathy

481

11

Optic Nerve and Glaucoma

483

 

Papilledema

483

 

Idiopathic Intracranial Hypertension (Pseudotumor Cerebri)

485

 

Optic Neuritis

486

 

Papillitis

486

 

Retrobulbar

486

 

Devic’s Syndrome

487

 

Anterior Ischemic Optic Neuropathy

488

 

Artcritic

488

 

Nonarteritic

488

 

Traumatic Optic Neuropathy

491

 

Other Optic Neuropathies

493

 

Compressive

493

 

Hereditary

493

 

Infectious

494

 

Infiltrative

494

 

Ischemic

494

 

Nutritional

494

 

Toxic

495

 

Congenital Anomalies

496

 

Aplasia

497

 

Dysplasias

497

 

Coloboma

497

 

Hypoplasia

497

 

Morning Glory Syndrome

498

 

Optic Nerve Drusen

498

 

Pit

499

 

Septo-Optic Dysplasia (De Morsier Syndrome)

500

 

Tilted Optic Disc

500

 

Tumors

501

 

Angioma (Von Hippel Lesion)

501

 

Astrocytic Hamartoma

501

 

Combined Hamartoma of Retina and Retinal Pigment Epithelium

501

 

Glioma

502

 

Melanocytoma

502

 

Meningioma

503

 

Chiasmal Syndromes

505

 

Congenital Glaucoma

508

 

Primary Open-Angle Glaucoma

509

 

Secondary Open-Angle Glaucoma

517

 

Drug Induced

517

 

Intraocular Tumor

518

 

Traumatic

518

 

Uveitic

518

 

Normal (Low) Tension Glaucoma

520

12

Visual Acuity, Refractive Procedures and Sudden Vision Loss

523

 

Refractive Error

523

 

Ametropia

523

 

Anisometropia

523

 

Astigmatism

523

 

Emmetropia

524

 

Hyperopia (Farsightedness)

524

 

Myopia (Nearsightedness)

524

 

Presbyopia

524

 

Refractive Surgery Complications

526

 

Intraocular Refractive Procedures

526

 

Clear Lens Extraction (Refractive Lens Exchange)

526

 

Phakic Intraocular Lens

526

 

Corneal Refractive Procedures

527

 

Incisional

527

 

Excimer Laser

528

 

Implants

532

 

Thermokeratoplasty

533

 

Refractive Surgery Complications: Evaluation/Management

533

 

Vertebrobasilar Insufficiency (Vertebrobasilar Atherothrombotic Disease)

535

 

Migraine

536

 

Migraine without Aura

536

 

Migraine with Aura

536

 

Childhood Periodic Syndromes

537

 

Retinal Migraine

537

 

Complications of Migraine

537

 

Convergence Insufficiency

538

 

Accommodative Excess (Accommodative Spasm)

539

 

Functional Visual Loss

540

 

Malingering

540

 

Hysteria

540

 

Transient Visual Loss (Amaurosis Fugax)

541

 

Amblyopia

542

 

Strabismic

542

 

Anisometropic

542

 

Isoametropic

543

 

Deprivation

543

 

Occlusion

543

 

Cortical Blindness (Cortical Visual Impairment)

544

 

Visual Pathway Lesions

544

 

Appendix

549

 

Ophthalmic History and Examination

549

 

History

549

 

Ocular Examination

549

 

Vision

549

 

Refraction

552

 

Retinoscopy

553

 

Lensometer

553

 

Potential Acuity Meter

554

 

Contrast Sensitivity

554

 

Color Vision

555

 

Stereopsis

555

 

4D Base Out Prism Test

556

 

Worth 4Dot Test

556

 

Ocular Motility

556

 

Cover Tests

557

 

Corneal Light Reflex Tests

559

 

Forced Ductions

560

 

Optokinetic Testing

560

 

Pupils

561

 

Visual Fields

561

 

Amsler Grid

562

 

Tangent Screen

562

 

Goldmann Visual Field

562

 

Humphrey Visual Field

563

 

External Examination

563

 

Exophthalmometry

563

 

Schirmer’s Test

564

 

Jones’ Dye Tests

564

 

Other Cranial Nerve Examination

564

 

Slit Lamp Examination

565

 

Dyes

566

 

Gonioscopy

566

 

Fundus Contact and Noncontact Lenses

567

 

Tonometry

567

 

Specialized Tests

568

 

Pachymetry

568

 

Keratometry

569

 

Corneal Topography

570

 

Wavefront Aberrometry

570

 

Specular Microscopy

570

 

Fundus Examination

571

 

Specialized Tests

573

 

Ultrasonography

573

 

Partial Coherence Laser Interferometry (Iolmaster)

574

 

Optical Coherence Tomography

574

 

AAO Suggested Routine Eye Examination Guidelines

575

 

Differential Diagnosis of Common Ocular Symptoms

575

 

Blurred Vision

575

 

Eye Pain

577

 

Tearing

577

 

Discharge

577

 

Flashes of Light

577

 

Red Eye

577

 

Common Ophthalmic Medications

577

 

Anti-Infectives

577

 

Antibiotics

577

 

Antiamoebics

580

 

Antifungals

580

 

Antivirals

581

 

Antiinflammatories

581

 

NSAIDs

581

 

Immunomodulator

581

 

Steroids

581

 

Ocular Hypotensive (Glaucoma) Medications

582

 

Alpha-Adrenergic Receptor Agonists

582

 

Beta-Blockers

582

 

Cholinergic Agonists (Miotics)

582

 

Carbonic Anhydrase Inhibitors

583

 

Prostaglandin Analogues

583

 

Hyperosmotics

583

 

Combinations

583

 

Allergy Medications

583

 

Mydriatics/Cydoplegics

584

 

Anesthetics

584

 

Miscellaneous

585

 

Artificial Tear Gel Formulations

585

 

Artificial Tear Solution Formulations

585

 

Color Codes for Topical Ocular Medication Caps

586

 

Ocular Toxicology

586

 

List of Important Ocular Measurements

587

 

List of Eponyms

588

 

Common Ophthalmic Abbreviations

591

 

Common Spanish Phrases

593

 

Suggested Readings

595

 

Index

597