Table of Contents

 

 

 

 

Contributing Authors

v

 

Preface

vii

 

Acknowledgments

ix

 

Introduction

xiii

1

The Basic Defect   Daniel J. Weiner, Raymond A. Frizzell, and David M. Orenstein

1

2

Making the Diagnosis   Jonathan E. Spahr, David M. Orenstein, and Daniel J. Weiner

13

3

The Respiratory System   Daniel J. Weiner and David M. Orenstein

21

4

The Gastrointestinal Tract   Douglas S. Lindblad, Daniel J. Weiner, and David M. Orenstein

83

5

Other Systems   Daniel J. Weiner and David M. Orenstein

103

6

Nutrition   Judith A. Fulton, Iris Yann, Daniel J. Weiner, and David M. Orenstein

113

7

Hospitalization and Other Special Treatments   Jonathan E. Spahr, David M. Orenstein, Daniel J. Weiner, and Louise T. Bauer

135

8

Transplantation   Geoffrey Kurland, Jonathan E. Spahr, Daniel J. Weiner, and David M. Orenstein

153

9

Daily Life   Jonathan E. Spahr, David M. Orenstein, and Daniel J. Weiner

195

10

Exercise   David M. Orenstein and Daniel J. Weiner

205

11

Genetics   Barbara Karczeski, Garry R. Cutting, and David M. Orenstein

221

12

The Family   David M, Orenstein and Daniel J. Weiner

235

13

The Teenage Years   Jonathan E. Spahr, David M. Orenstein, and Daniel J. Weiner

245

14

Cystic Fibrosis and Adulthood   Joseph M. Piliewski, David M. Orenstein, Jonathan E. Spahr, and Daniel J. Weiner

265

15

Death and Cystic Fibrosis   Elisabeth P. Dellon and David M. Orenstoin

287

16

Research and Future Treatments   Christopher Penland, David M. Orenstein, and Daniel J. Weiner

295

17

The Cystic Fibrosis Foundation   Robert J. Beall

311

 

APPENDICES

 

A

Glossary of Terms

319

B

Medications

325

C

Airway Clearance Techniques

363

D

Some High Calorie Recipes

375

E

The History of Cystic Fibrosis

385

F

Bibliography and Resources

387

G

Cystic Fibrosis Care Centers in the United States

391

H

Cystic Fibrosis Care Centers Worldwide

411

 

Index

445